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Guidelines Into Practice
Pulmonary Hypertension

Pulmonary Hypertension (Guidelines on Diagnosis and Treatment of)

ESC Clinical Practice Guidelines

Congenital Heart Disease and Pediatric Cardiology
Epidemiology, Prognosis, Outcome
Pulmonary Hypertension
Valvular Heart Disease
Chronic Heart Failure
Pulmonary Circulation, Pulmonary Embolism, Right Heart Failure
Guidelines version available to download
Published in 2015
Reference European Heart Journal 2016:37;67–119 -doi:10.1093/eurheartj/ehv317
Published in 2015
Reference Web Addenda
Published in 2015
Reference CME Questions - Pulmonary Hypertension
Published in 2015
Reference Pulmonary Hypertension Pocket Guidelines
Published in 2017
Reference 51 Slides
Published in 2015
Reference ESC Pocket Guidelines App
Published in 2015
Reference Key Messages and Gaps in Evidence
Published in 2009
Reference European Heart Journal (2009) 30, 2493–2537; doi:10.1093/eurheartj/ehp297
Table of contents: Full Text (ESC Clinical Practice Guidelines)

1. Preamble
2. Introduction
3. Definitions and classifications
3.1 Definitions
3.2. Classifications
4. Epidemiology and genetics of pulmonary hypertension
4.1 Epidemiology and risk factors
4.2 Genetics
5. Pulmonary hypertension diagnosis
5.1 Diagnosis
5.1.1 Clinical presentation
5.1.2 Electrocardiogram
5.1.3 Chest radiograph
5.1.4 Pulmonary function tests and arterial blood gases
5.1.5 Echocardiography
5.1.6 Ventilation/perfusion lung scan
5.1.7 High-resolution computed tomography, contrast enhanced computed tomography, and pulmonary angiography
5.1.8 Cardiac magnetic resonance imaging
5.1.9 Blood tests and immunology
5.1.10 Abdominal ultrasound scan
5.1.11 Right heart catheterization and vasoreactivity
5.1.12 Genetic testing
5.2 Diagnostic algorithm
6. Pulmonary arterial hypertension (group 1)
6.1 Clinical characteristics
6.2 Evaluation of severity
6.2.1 Clinical parameters, imaging and haemodynamics
6.2.2 Exercise capacity
6.2.3 Biochemical markers
6.2.4 Comprehensive prognostic evaluation and riskassessment
6.2.5 Definition of patient status
6.2.6 Treatment goals and follow-up strategy
6.3 Therapy
6.3.1 General measures
6.3.2 Supportive therapy
6.3.3 Specific drug therapy
6.3.4 Combination therapy
6.3.5 Drug interactions
6.3.6 Balloon atrial septostomy
6.3.7 Advanced right ventricular failure
6.3.8 Transplantation
6.3.9 Treatment algorithm
6.3.10 Diagnosis and treatment of pulmonary arterial hypertension complications  
6.3.11 End of life care and ethical issues
7. Specific pulmonary (arterial) hypertension subsets
7.1 Paediatric pulmonary arterial hypertension
7.1.1 Diagnosis
7.1.2 Therapy
7.2 Pulmonary arterial hypertension associated with adult congenital heart disease
7.2.1 Diagnosis
7.2.2 Therapy
7.3 Pulmonary arterial hypertension associated with connective tissue disease
7.3.1 Diagnosis
7.3.2 Therapy
7.4 Pulmonary arterial hypertension associated with portal hypertension
7.4.1 Diagnosis
7.4.2 Therapy
7.5 Pulmonary arterial hypertension associated with human immunodeficiency virus infection
7.5.1 Diagnosis
7.5.2 Therapy
7.6 Pulmonary veno-occlusive disease and pulmonary capillary haemangiomatosis
7.6.1 Diagnosis
7.6.2 Therapy
8. Pulmonary hypertension due to left heart disease (group 2)
8.1 Diagnosis
8.2 Therapy
9. Pulmonary hypertension due to lung diseases and/or hypoxia (group 3)
9.1 Diagnosis
9.2 Therapy
10. Chronic thromboembolic pulmonary hypertension (group 4)
10.1 Diagnosis
10.2 Therapy
10.2.1 Surgical
10.2.2 Medical
10.2.3 Interventional
11. Pulmonary hypertension with unclear and/or multifactorial mechanisms (group 5)
12. Definition of a pulmonary hypertension referral centre
13. To do and not to do messages from the guidelines
14. Appendix
15. Web addenda
16. References

Previous version available to download
Published in 
Reference doi:10.1093/eurheartj/ehr046