Pocket Guidelines on Pulmonary Hypertension

Publication date: 2022
Chairpersons: Stephan Rosenkranz and Marion Delcroix 

Table of Contents

1. Introduction

2. Methods

3. Definitions and classifications

3.1. Definitions

3.2. Classifications

4. Epidemiology and risk factors

5. Pulmonary hypertension diagnosis

5.1. Diagnosis

5.2. Diagnostic algorithm

5.3. Screening and early detection

6. Pulmonary arterial hypertension (group

6.1. Clinical characteristics

6.2. Severity and risk assessment

6.3. Therapy

7. Specific pulmonary arterial hypertension subsets

7.1. Pulmonary arterial hypertension associated with drugs and toxins

7.2. Pulmonary arterial hypertension associated with connective tissue disease

7.3. Pulmonary arterial hypertension associated with human

immunodeficiency virus infection

7.4. Pulmonary arterial hypertension associated with portal hypertension

7.5. Pulmonary arterial hypertension associated with adult congenital

heart disease

7.6. Pulmonary arterial hypertension with signs of venous/capillaries

involvement

7.7. Paediatric pulmonary hypertension

8. Pulmonary hypertension associated with left heart disease (group 2)

8.1. Definition, prognosis, and pathophysiology

8.2. Diagnosis

8.3. Therapy

9. Pulmonary hypertension associated with lung diseases and/or hypoxia (group 3)

9.1. Diagnosis

9.2. Therapy

10. Chronic thrombo-embolic pulmonary hypertension (group 4)

10.1. Diagnosis

10.2. Therapy.

11. Pulmonary hypertension with unclear and/or multi-factorial mechanisms

(group 5)

12. Definition of a pulmonary hypertension centre

12.1. Facilities and skills required for a pulmonary hypertension centre

12.2. Patient associations and patient empowerment