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Pulmonary Hypertension (Guidelines on Diagnosis and Treatment of)

ESC Clinical Practice Guidelines

Pulmonary Disease
Pulmonary Hypertension
Valvular Heart Diseases
Guidelines version available to download
Published in 2015
Reference 2015 Guidelines on Pulmonary Hypertension
Published in 2015
Reference Web Addenda
Published in 2015
Reference CME Questions - Pulmonary Hypertension
Published in 2015
Reference Pulmonary Hypertension Pocket Guidelines
  • PDA
  • Published in 2015
    Reference ESC Pocket Guidelines App
    Published in 2015
    Reference Key Messages and Gaps in Evidence
    Published in
    Reference doi:10.1093/eurheartj/ehr046
    Published in 2009
    Reference European Heart Journal (2009) 30, 2493–2537; doi:10.1093/eurheartj/ehp297
    Authors

    Nazzareno Galiè  (ESC Chairperson) (Italy),Marc Humbert(ERS Chairperson) (France), Jean-Luc Vachieryc (Belgium), Simon Gibbs (UK), Irene Lang (Austria), AdamTorbicki (Poland), Gerald Simonneau (France), Andrew Peacock (UK), Anton Vonk Noordegraaf (The Netherlands), Maurice Beghetti (Switzerland), Ardeschir Ghofrani (Germany),Miguel Angel Gomez Sanchez (Spain), Georg Hansmann (Germany)

    Endorsed by cardiac societies
    Table of contents: Full Text (ESC Clinical Practice Guidelines)

    Table of contents: Full Text (ESC Clinical Practice Guidelines)


    1. Preamble
    2. Introduction
    3. Definitions and classifications
    3.1 Definitions
    3.2. Classifications
    4. Epidemiology and genetics of pulmonary hypertension
    4.1 Epidemiology and risk factors
    4.2 Genetics
    5. Pulmonary hypertension diagnosis
    5.1 Diagnosis
    5.1.1 Clinical presentation
    5.1.2 Electrocardiogram
    5.1.3 Chest radiograph
    5.1.4 Pulmonary function tests and arterial blood gases
    5.1.5 Echocardiography
    5.1.6 Ventilation/perfusion lung scan
    5.1.7 High-resolution computed tomography, contrast enhanced computed tomography, and pulmonary angiography
    5.1.8 Cardiac magnetic resonance imaging
    5.1.9 Blood tests and immunology
    5.1.10 Abdominal ultrasound scan
    5.1.11 Right heart catheterization and vasoreactivity
    5.1.12 Genetic testing
    5.2 Diagnostic algorithm
    6. Pulmonary arterial hypertension (group 1)
    6.1 Clinical characteristics
    6.2 Evaluation of severity
    6.2.1 Clinical parameters, imaging and haemodynamics
    6.2.2 Exercise capacity
    6.2.3 Biochemical markers
    6.2.4 Comprehensive prognostic evaluation and riskassessment
    6.2.5 Definition of patient status
    6.2.6 Treatment goals and follow-up strategy
    6.3 Therapy
    6.3.1 General measures
    6.3.2 Supportive therapy
    6.3.3 Specific drug therapy
    6.3.4 Combination therapy
    6.3.5 Drug interactions
    6.3.6 Balloon atrial septostomy
    6.3.7 Advanced right ventricular failure
    6.3.8 Transplantation
    6.3.9 Treatment algorithm
    6.3.10 Diagnosis and treatment of pulmonary arterial hypertension complications  
    6.3.11 End of life care and ethical issues
    7. Specific pulmonary (arterial) hypertension subsets
    7.1 Paediatric pulmonary arterial hypertension
    7.1.1 Diagnosis
    7.1.2 Therapy
    7.2 Pulmonary arterial hypertension associated with adult congenital heart disease
    7.2.1 Diagnosis
    7.2.2 Therapy
    7.3 Pulmonary arterial hypertension associated with connective tissue disease
    7.3.1 Diagnosis
    7.3.2 Therapy
    7.4 Pulmonary arterial hypertension associated with portal hypertension
    7.4.1 Diagnosis
    7.4.2 Therapy
    7.5 Pulmonary arterial hypertension associated with human immunodeficiency virus infection
    7.5.1 Diagnosis
    7.5.2 Therapy
    7.6 Pulmonary veno-occlusive disease and pulmonary capillary haemangiomatosis
    7.6.1 Diagnosis
    7.6.2 Therapy
    8. Pulmonary hypertension due to left heart disease (group 2)
    8.1 Diagnosis
    8.2 Therapy
    9. Pulmonary hypertension due to lung diseases and/or hypoxia (group 3)
    9.1 Diagnosis
    9.2 Therapy
    10. Chronic thromboembolic pulmonary hypertension (group 4)
    10.1 Diagnosis
    10.2 Therapy
    10.2.1 Surgical
    10.2.2 Medical
    10.2.3 Interventional
    11. Pulmonary hypertension with unclear and/or multifactorial mechanisms (group 5)
    12. Definition of a pulmonary hypertension referral centre
    13. To do and not to do messages from the guidelines
    14. Appendix
    15. Web addenda
    16. References


     

     

     

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    European Society
    of Cardiology

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